Schwannomas generally occur in the head, neck, and extremities; however, its occurrence in the retroperitoneal pelvic space is rare. Here, we describe four successful surgical managements of retroperitoneal pelvic schwannoma which was identified in preoperative imaging studies. Computed tomography demonstrated heterogeneous masses in the retroperitoneum with well-defined margins. The retroperitoneal pelvic schwannomas were removed by complete excision or enucleation through either laparotomy or laparoscopy. The diagnoses of schwannoma were further confirmed via histopathology. Postoperatively, two patients had transient but minimal neurologic deficits in a lower extremity. No evidence of tumor recurrence was detected over a 12-month following-up of four patients. A meticulous review of three-dimensional imaging studies provided correct preoperative diagnoses of schwannomas. Postoperative neurologic deficits may be less serious than expected. Complete resection of the tumor is the treatment of choice, and recurrence is unusual.
