IMR Press / EJGO / Volume 39 / Issue 6 / DOI: 10.12892/ejgo4241.2018

European Journal of Gynaecological Oncology (EJGO) is published by IMR Press from Volume 40 Issue 1 (2019). Previous articles were published by another publisher on a subscription basis, and they are hosted by IMR Press on imrpress.com as a courtesy and upon agreement with S.O.G.

Open Access Case Report
Intrapelvic sclerosing epithelioid fibrosarcoma: a case report
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1 Department of Obstetrics and Gynecology, Faculty of Medicine, University of Yamanashi, Japan
2 Department of Radiology, Faculty of Medicine, University of Yamanashi, Yamanashi, Japan
3 Department of Pathology, Faculty of Medicine, University of Yamanashi, Yamanashi, Japan
Eur. J. Gynaecol. Oncol. 2018, 39(6), 1028–1031; https://doi.org/10.12892/ejgo4241.2018
Published: 10 December 2018
Abstract

Sclerosing epithelioid fibrosarcoma (SEF) is a rare deep-seated tumor, that typically develops in the lower extremity, limb girdle, and trunk. This tumor is clinically aggressive, with a poor prognosis. The authors present an extremely rare case of SEF developing in the pelvis. The patient was a 75-year-old woman presenting with a solid mass located adjacent to the uterus in the left adnexal region on vaginal ultrasonography. MRI showed a lobulated solid mass exhibiting hypointensity on T1- and T2-weighted imaging. The tumor also showed heterogeneous signal intensity on diffusion-weighted imaging, and heterogeneous enhancement on dynamic study, and both features were distinct in the tumor’s peripheral zone. These MRI features were correlated with more hypercellularity in the peripheral zone on histology. To date, few reports have focused on the MRI features of SEF. Diffusion-weighted and contrast-enhanced MRI may provide more useful information for the diagnosis of SEF located in uncommon sites.
Keywords
Fibrosarcoma
Sclerosing epithelioid fibrosarcoma
Pelvic mass
Magnetic resonance imaging
Immunohistochemistry
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