IMR Press / EJGO / Volume 33 / Issue 1 / pii/1631086204267-1733347170

European Journal of Gynaecological Oncology (EJGO) is published by IMR Press from Volume 40 Issue 1 (2019). Previous articles were published by another publisher on a subscription basis, and they are hosted by IMR Press on imrpress.com as a courtesy and upon agreement with S.O.G.

Open Access Case Report
Desmoplastic small round cell tumor (DSRCT) arising in the ovary: report of a case diagnosed at an early stage and review of the literature
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1 Department of Obstetrics and Gynecology, University of Modena and Reggio Emilia, Modena (Italy)
2 Department of Gynecological Oncology, University Multidisciplinary Breast and Pelvic Gynecological Oncology Clinic, Antwerp University Hospital, Edegem
3 Department of Medical Oncology, University Multidisciplinary Breast and Pelvic Gynecological Oncology Clinic, Antwerp University Hospital, Edegem (Belgium)
Eur. J. Gynaecol. Oncol. 2012, 33(1), 96–100;
Published: 10 February 2012
Abstract

Background: Desmoplastic small round cell tumor (DSRCT) is a rare sarcoma tumor affecting mainly young adult males. It rarely has an ovarian involvement. Case: A 29-year-old woman presented to her gynecologist for amenorrhoea. The laboratory results demonstrated a menopausal status and the ultrasound revealed a large mass of the right ovary. The right ovary was completely removed by laparoscopy. Pathology, cytology and immunochemistry revealed a DSRCT. In January 2009 a left salpingo-oophorectomy and a right salpingectomy were performed via laparoscopy. After 35 months from diagnosis there was no clinical evidence of disease recurrence. Conclusion: DSRCT is a rare ovarian tumor in adolescence with a general poor outcome. Every ovarian mass regardless of age should be approached with caution.
Keywords
Desmoplastic small round cell tumor
Ovarian neoplasm
Early stage tumor
Treatment
Good response
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