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European Journal of Gynaecological Oncology (EJGO) is published by IMR Press from Volume 40 Issue 1 (2019). Previous articles were published by another publisher on a subscription basis, and they are hosted by IMR Press on imrpress.com as a courtesy and upon agreement with S.O.G.
Retroperitoneal primitive neuroectodermal tumor (PNET): case report and review of literature
A. Koch1, *, S. Frigo1, L. Lecointre1, M. Hummel1, C.Y. Akladios1, J.P. Bergerat2, G. Noël Noël3, A. Wattiez1
1 Department of Obstetrics and Gynecology, Strasbourg University Hospital, Schiltigheim, France
2 Department of Oncology and Hematology, Strasbourg University Hospital, Strasbourg Cedex, France
3 Department of Radiotherapy, Centre de lutte contre le cancer Paul Strauss, Strasbourg, France
Eur. J. Gynaecol. Oncol. 2017, 38(2), 314–318; https://doi.org/10.12892/ejgo3510.2017
Published: 10 April 2017
Primitive Neuroectodermal tumor belongs to the family of Ewing’s tumor and is characterized by a t (11;22) (q24;q12) or a t (21;22) (q22;q12) translocation. Retroperitoneal primitive neuroectodermal tumor (PNET) are rare, usually affect young adults, and are often diagnosed late. There is no specific characteristics for imaging. The diagnosis is made on histological examination of the surgical specimen or biopsies. Radiotherapy and chemotherapy complete the treatment. The authors report the case of a 26-year-old patient who only had pelvic discomfort. Diagnostic laparoscopy showed a retroperitoneal and retrovesical mass of five centimeters. The patient benefited from adjuvant chemotherapy and radiotherapy. She is free of disease 30 months after treatment.
Primitive neuroectodermal tumor