IMR Press / CEOG / Volume 41 / Issue 6 / DOI: 10.12891/ceog18022014

Clinical and Experimental Obstetrics & Gynecology (CEOG) is published by IMR Press from Volume 47 Issue 1 (2020). Previous articles were published by another publisher on a subscription basis, and they are hosted by IMR Press on imrpress.com as a courtesy and upon agreement with S.O.G.

Case Report
Psychosexual and social consequences in a woman with undiagnosed Mayer-Rokitansky-Küster-Hauser syndrome
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1 Department of Obstetrics and Gynecology, King Abdulaziz University, Jeddah (Saudi Arabia)
Clin. Exp. Obstet. Gynecol. 2014, 41(6), 734–735; https://doi.org/10.12891/ceog18022014
Published: 10 December 2014
Abstract

Purpose: To report a woman with devastating psychosexual and social consequences as a result of undiagnosed Mayer-Rokitansky- Küster-Hauser syndrome (MRKH) syndrome. Materials and Methods: An 18-year-old woman was referred after being divorced for “absent vagina and uterus”. On examination, secondary sexual characteristics were normal. Vaginal and rectal examinations revealed absent vagina and uterus. Investigations showed normal hormonal profile, 46 XX karyotype, and normal intravenous pyelography. Pelvic ultrasonography and magnetic resonance imaging (MRI) confirmed the absence of the uterus and presence bilateral ovaries. Results: A diagnosis of MRKH syndrome was made and she underwent successful modified laparoscopic Vecchietti operation for creation of a new vagina. Vaginal dilators were used after the surgery. Two years of follow up confirmed that vaginal length was about ten cm. Conclusion: The proper diagnosis, counseling, and prompt treatment of MRKH syndrome can prevent tragic consequences.
Keywords
Intercourse
Mayer-Rokitansky-Küster-Hauser syndrome
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